Inflammatory myofibroblastic tumor. An aggressive case report

Authors

  • Héctor Ayerra-Pérez Osakidetza, Hospital Universitario Araba, Vitoria-Gasteiz, España.
  • Natalia Herrera Aranda Osakidetza, Hospital Universitario Araba, Vitoria-Gasteiz, España.
  • Erika Iglesias-Martínez Osakidetza, Hospital Universitario Araba, Vitoria-Gasteiz, España.
  • Javier Extramiana-Cameno Osakidetza, Hospital Universitario Araba, Vitoria-Gasteiz, España.

DOI:

https://doi.org/10.48193/revistamexicanadeurologa.v82i6.923

Keywords:

Inflammatory Myofibroblastic Tumor, Inflammatory Pseudotumor, Inflammatory Fibrosarcoma, Plasma Cell Granuloma, Anaplastic Lymphoma kinase Inhibitors

Abstract

Clinic case: We present an extraordinary case report from a male diagnosed with Inflammatory Myofibroblastic Tumors (IMT) after suddenly presenting with a haemorrhagic shock due to hematuria. He underwent a partial cystectomy to achieve the complete resection and confirm the pathologic diagnosis. After the complete resection, he is free of relapse.

Relevance: Our case report shows an extraordinary aggressiveness and a life-threatening disease course. The final pathologic exam confirmed the diagnosis and reported the pathologic correlation with the radiological findings of such an infrequent entity.

Clinical implications: Although infrequent, IMT might present aggressively. After the initial clinical and radiological suspicion, finding must be confirmed by the complete resection and the pathologic exam.

Conclusion: The early diagnosis enables the complete resection of the tumor, which is the most determinant prognostic factor. Selected patients with unresectable lesions might also benefit from adjuvant treatment with ALK-inhibitors.

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Published

2023-01-13

Issue

Vol. 82 No. 6 (2022): November-December

Section

Clinical cases

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