Zinner syndrome: an up-to-date literature review based on an asymptomatic clinical case
DOI:
https://doi.org/10.48193/revistamexicanadeurologa.v80i5.620Keywords:
Zinner syndrome, monoreneum, seminal vesicle cyst, mesonephric ductsAbstract
Clinical case description: A 38-year-old man initially presented with anuria secondary to a right solitary kidney and a stone in the lower third of the ureter that was resolved through laser ureterolithotripsy. As part of his evaluation, extension studies were performed that identified a cyst in the left seminal vesicle.
Relevance: Due to the mutual embryologic origins of the seminal vesicle, vas deferens, and ureteric bud, developmental alterations of the mesonephric duct (Wolffian duct) and the absence of the ureteric bud during the first trimester of gestation are associated with ipsilateral renal agenesis and ejaculatory duct atresia that will later progress to cystic dilation of the seminal vesicle.
Conclusions: Zinner syndrome was first described in 1914 and it continues to be a rare condition worldwide. In fact, only approximately 200 cases have been reported in the literature.
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