Metastatic Wilms' tumor in young adult: case report
DOI:
https://doi.org/10.48193/069ehc32Keywords:
: tumor de wilms, nefroblastomaAbstract
Clinical case: a 20-year-old male patient with type 1 obesity presents with abdominal and dorsal pain. Pathological diagnosis reported Wilms tumor (WT) stage IV. He received preoperative chemotherapy and subsequently underwent left radical nephrectomy. Currently, the patient remains asymptomatic and without evidence of recurrence 12 months after surgery.
Relevance: Wilms tumor or nephroblastoma is an uncommon pathology in the adult population with very few reported cases. The advanced stage of the disease complicates surgical and oncologic treatment.
Medical implications: currently, there are no defined guidelines for the treatment of WT in the adult population due to its low frequency and the lack of information on the strategies employed in high-specialty hospitals where these cases have been managed.
Conclusions: the therapeutic approach of WT in adults presents significant challenges, making it necessary to establish a standardized model of care and management. The partial response to chemotherapy and the appearance of new lesions indicates the possibility of requiring additional treatments, as well as strict surveillance. Systematic recording and analysis of these cases will contribute to the development of more effective therapeutic strategies for this rare clinical entity.
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