Persistant fetal lobulation associated with kidney malrotation: a case report and review of current literature
DOI:
https://doi.org/10.48193/revistamexicanadeurologa.v83i5.1062Keywords:
Congenital anomalies of the kidneys and urinary tract (CAKUT), urinary tract, urogenital abnormalities, MAPK kinaseAbstract
A patient came to emergency services with symptoms of pyelonephritis; she has a right nephrectomy due to severe hydronephrosis. In her workup MRI showed nephromegaly, persistent fetal lobulation and kidney malrotation; uroanalysis and urinary culture showed urinary infection cause by E. coli. With these findings pyelonephritis was confirmed and she was treated with antibiotics.
Nowadays we don’t have absolute knowledge of the cause for these malformations but studies have found an alteration on the protein-kinase pathway. It is important to recognize these malformations because of its association with others can increase the risk of complications. It is advisable to identify them in early ages to avoid incorrect diagnosis and to prevent complications in future.
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